一例43歲的女性馬凡綜合征患者，主訴進行性呼吸困難和胸痛2小時來診，她於5年前接受了升主動脈夾層修複術。生命體征正常，無心血管、神經或腎功能異常。CT檢查確診為始於主動脈根部的非常複雜的主動脈夾層(A圖)，下至兩側髂動脈(E圖)，上至兩側頸動脈(F圖)，一個小的閉塞真腔至腎動脈和髂動脈(圖C和E)。經胸超聲心動圖檢查顯示，主動脈根部擴張，夾層組織下垂至升主動脈、正常主動脈瓣和幾乎被擴張的降主動脈和巨大血栓閉塞的左心耳(圖G和H)。

患者在專科診療中心接受了緊急外科手術，行主動脈複雜修複術和外周動脈的修複術，無任何神經或終末器官損害，恢複良好。

原文：

CT and TTE Imaging Reveal a Complex Aortic Dissection in a Patient With Marfan Syndrome | Clinical Images

Apr 21, 2015 | Kusum Lata, MD

A 43-year-old woman with Marfan syndrome who underwent ascending aortic dissection repair five years ago presents with progressive dyspnea and chest pain for two hours. Her vital signs were normal, and there was no cardiovascular, neurological, or renal dysfunction. Computed tomographic examination of the body confirmed a very complex aortic dissection starting from the aortic root (Figure A), below to bilateral iliac arteries (Figure E) and upwards to both carotid arteries (Figure F). A small obliterated true lumen feeding the renal and iliac arteries is displayed in Figure C and E. Transthoracic echocardiogram revealed enlarged aortic root with dissection flap in ascending aorta, normal aortic valve, and almost obliterated left atrium by dilated descending aorta and large thrombus burden (Figures G, H). The patient underwent urgent surgery at specialized center. Complex repair of the aorta and peripheral arteries was performed, and she is recuperating well without any neurological or end organ deficit.